Auditory neuropathy spectrum disorder

Auditory neuropathy spectrum disorder (ANSD) is a specific form of hearing loss defined by the presence of normal or near-normal otoacoustic emissions (OAEs) but the absence of normal middle ear reflexes and severely abnormal or completely absent auditory brainstem response (ABRs).

Early diagnosis of auditory neuropathy spectrum disorder (ANSD) in children is critical for timely intervention and optimal speech and language acquisition and development[1]. Guidelines for the diagnosis and management of auditory neuropathy spectrum disorderIndividuals presenting with this recently recognised hearing loss appear to display sporadic windows of hearing and not. Very few (1 in 14) will go on to develop normal speech and language but with poor speech perception in background noise and in others, no speech perception and therefore language development is possible.

The condition was originally termed auditory neuropathy (AN)[2] and in 2001 as Auditory Neuropathy / Auditory Dys-synchrony (AN/AD)[3] (to include those cases where no true neuropathy was apparent). In 2008 at a meeting convened at Lake Como in Italy (Guidelines Development Conference on the Identification and Management of Infants with Auditory Neuropathy, International Newborn Hearing Screening Conference, Como, Italy, June 19–21, 2008), a group of leading authorities on the condition reached a consensus and renamed it as auditory neuropathy spectrum disorder.[4]

See also

References

  1. ↑ "Early Hearing Detection and Intervention". American Speech-Language-Hearing Association. Retrieved 2026-03-24.
  2. ↑ Starr, A.; Picton, T.W.; Sininger, Y.; Hood, L.J.; Berlin, C.I. (1996). "Auditory neuropathy". Brain. 119 (3): 741–753. doi:10.1093/brain/119.3.741. PMID 8673487.
  3. ↑ Berlin, C.I.; Hood, L.J.; Rose, K. (2001). "On renaming auditory neuropathy as auditory dys-synchrony" (PDF). Audiology Today. 13: 15–17. Archived from the original (PDF) on 2020-11-24. Retrieved 2020-06-26.
  4. ↑ Berlin, CI; Morlet, T; Hood, LJ (2008). "Management of individuals with auditory neuropathy spectrum disorder". Guidelines for Identification and Management of Infants and Young Children with Auditory Neuropathy Spectrum disorder. Bill Daniels Center for Children’s Hearing: 35–40.


This page is issued from Wikipedia. The text is available under Creative Commons Attribution-Share Alike 4.0 unless otherwise noted. Additional terms may apply for the media files.